Pulmonary hypertension syndrome secondary to right atrial myxoma apropos of a case
Abstract
Atrial myxoma is a benign primary cardiac tumor that is mostly found in the left atrium. This paper aims to describe the clinical presentation of a right atrial myxoma through the case report of a 54-year-old patient diagnosed with pulmonary hypertension syndrome secondary to the above-mentioned cardiac tumor. The clinical features of myxomas are determined by their location, size and mobility. In this case, intracardiac obstruction produced by the myxoma, with paradoxical movement of the septum, resulted in ventricular filling alterations, low cardiac output signs and severe pulmonary hypertension. Immediate clinical and surgical management after diagnosis successfully prevented the development of major complications. This case highlights the paramount importance of clinical judgment and the use of various cardiac imaging techniques in decision making.Downloads
References
1. Muñoz Serret D, García E, Páez J, Hernández E. Mixoma gigante de aurícula derecha. Presentación de un caso. Cir Cardiov. 2013;20(4):203-5.
2. Arauz A, Cantú C, Merlos Benítez M, Hernández-Curiel B, Barinagarrementeria F, Roldán J. Enfermedad cerebrovascular como complicación de mixoma auricular. Reporte de seis casos y revisión de la literatura. Rev Mex Neuroci. 2010;11(3):194-8.
3. Lenihan DJ, Yusuf SW. Tumores que afectan al sistema cardiovascular. En: Mann DL, Zipes DP, Libby P, Bonow RO, eds. Braunwald, Tratado de Cardiología: Texto de medicina cardiovascular. 10ª ed. Barcelona: Elsevier; 2016. p. 1863-75.
4. Solórzano-Morales SA, de Rubens-Figueroa J, Palacios Macedo-Quenot A, Bernal-Moreno MA, Corchera-Delgado CT, Gómez-Garza G. Tromboembolia sistémica originada por un mixoma auricular izquierdo en un adolescente. Acta Pediatr Mex. 2011;32(3):183-9.
5. Leja MJ, Shah DJ, Reardon MJ. Primary cardiac tumors. Tex Heart Inst J. 2011;38(3):261-2.
6. Panidis IP, Kotler MN, Mintz GS, Ross J. Clinical and echocardiographic features of right atrial masses. Am Heart J. 1984;107(4):745-58.
7. Hoffmeier A, Sindermann JR, Scheld HH, Martens S. Cardiac tumors – Diagnosis and surgical treatment. Dtsch Arztebl Int. 2014;111(12):205-11.
8. Motwani M, Kidambi A, Herzog BA, Uddin A, Greenwood JP, Plein S. MR imaging of cardiac tumors and masses: a review of methods and clinical applications. Radiology. 2013;268(1):26-43.
9. Villar Inclán A, Guevara González L, Nafeh Abiz-reck M, Chil Díaz R, Chaos González N. Mixomas cardíacos: análisis estadístico de 20 años. Rev Cuba Cir [Internet]. 2009 [citado 20 Feb 2019];48(4). Disponible en: http://scielo.sld.cu/pdf/cir/v48n4/cir02409.pdf
10. Castellanos Tardo J, de la Torre Fonseca CA, Machín Rodríguez JC, Torralbas Reverón F, Ávalos Carrazana G. Aspectos clínicos de los mixomas cardíacos. Primera serie de la región oriental de Cuba. MEDISAN [Internet].2010 [citado 22 Feb 2019];14(8):1083-90. Disponible en: http://scielo.sld.cu/pdf/san/v14n8/san06810.pdf
11. Medrano Plana Y, Vázquez Roque FJ, Lagomasino Hidalgo AL, Puig Reyes I, Hernández Borroto CE, Bermúdez Yera GJ, et al. Mixomas cardíacos. Resultados del tratamiento quirúrgico en 23 años de trabajo. Rev Electrón Portales Médicos.com [Internet]. 2010;5(6):127. Disponible en: https://www.portalesmedicos.com/publicaciones/articles/2081/1/Mixomas-cardiacos-Resultados-del-tratamiento-quirurgico-en-23-anos-de-trabajo.html
12. Masuda I, Ferreño AM, Pasca J, Pereiro G, Lastiri H. Tumores cardíacos primarios. Mixoma auricular. Rev Fed Arg Cardiol. 2004;33(2):196-204.
13. Bermúdez Yera R, Lagomasino Hidalgo A, Bermúdez Yera GJ, Medrano Plana Y, González Díaz A, Monteagudo Lima L, et al. Mixoma biauricular: Presentación del primer caso operado en el Cardiocentro Ernesto Che Guevara. CorSalud [Internet]. 2010 [citado 26 Feb 2019];2(2). Disponible en: http://www.corsalud.sld.cu/sumario/2010/v2n2a10/mixoma.htm
14. Villalpando-Mendoza E, Pérez-Pérez FM, Cortés-Flores AO, Velázquez-Ramírez GA, Fuentes-Orozco C, González-Ojeda A. Frecuencia de tumores cardiacos y su correlación histopatológica. Cir Cir. 2006;74(3):183-7.
15. Scholz J, Suárez C, Mota JD. Mixomas cardíacos: estudio morfológico e inmunohistoquímico de 50 biopsias. Gac Méd Caracas. 2007;115(2):126-37.
16. Rottier Salguero R, Vega Ulate GA. Tumor primario del corazón más común: mixoma cardíaco. Rev Méd Costa Rica Centroam. 2012;LXIX(604):481-7.
17. Lang IM, Pesavento R, Bonderman D, Yuan JX. Risk factors and basic mechanisms of chronic thromboembolic pulmonary hypertension: a current understanding. Eur Respir J. 2013;41(2):462-8.
18. Pepke-Zaba J, Jansa P, Kim NH, Naeije R, Simonneau G. Chronic thromboembolic pulmonary hypertension: role of medical therapy. Eur Respir J. 2013;41(4):985-90.
19. Kim N, Delcroix M, Jenkins DP, Channick R, Dartevelle P, Jansa P, et al. Chronic thromboembolic pulmonary hypertension. J Am Coll Cardiol. 2013;62(25 Supl D):92-9.
20. Galiè N, Humbert M, Vachiery JL, Gibbs S, Lang I, Torbicki A, et al. Guía ESC/ERS 2015 sobre diagnóstico y tratamiento de la hipertensión pulmonar. Rev Esp Cardiol. 2016;69(2):177.e1-e62.
21. Favaloro RR, Peradejordi MA, Gómez CB, Santos M, Caneva JO, Klein F, et al. Tromboendarterectomía pulmonar: tratamiento de elección para la hipertensión pulmonar tromboembólica crónica. Rev Am Med Resp. 2011;11(2):74-83.
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