Fragmented QRS and sudden death in a patient with arrhythmogenic right ventricular dysplasia/cardiomyopathy

Authors

  • Luis A. Rodríguez López
  • Eliany Rodríguez Moreno
  • Juan M. Cruz Elizundia
  • Yohan M. Díaz Sardiñas
  • Reinaldo Gavilanes Hernández
  • Ruben R. Quenta Tarqui
  • Jhosely A. González Achacollo
  • Carlos Santana Santana

Abstract

The arrhythmogenic right ventricular dysplasia or cardiomyopathy is a genetic heart disease whose diagnosis is often a challenge for the clinician. It is one of the most common causes of sudden cardiac death in adolescence and in young adults. We present the case of a patient with a history of malignant ventricular arrhythmias and recovered sudden cardiac death due to arrhythmogenic right ventricular dysplasia, with QRS fragmentation in the right precordial leads, as a marker of the presence of a suitable substrate for the emergence of spontaneous ventricular fibrillation. The pathogenesis, diagnosis and treatment of this disease are discussed.

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Published

2019-01-03

How to Cite

1.
Rodríguez López LA, Rodríguez Moreno E, Cruz Elizundia JM, Díaz Sardiñas YM, Gavilanes Hernández R, Quenta Tarqui RR, et al. Fragmented QRS and sudden death in a patient with arrhythmogenic right ventricular dysplasia/cardiomyopathy. CorSalud [Internet]. 2019 Jan. 3 [cited 2025 Sep. 11];11(1):70-4. Available from: https://revcorsalud.sld.cu/index.php/cors/article/view/440

Issue

Vol. 11 No. 1 (2019)

Section

CASE REPORTS

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