Left ventricular noncompaction apropos of a case

Authors

  • Alain Gutiérrez López Hospital ClínicoQuirúrgico Hermanos Ameijeiras. La Habana Cuba.
  • Carlos Ramos Emperador Hospital ClínicoQuirúrgico Hermanos Ameijeiras. La Habana Cuba.
  • Marleny Cruz Cardentey Hospital ClínicoQuirúrgico Hermanos Ameijeiras. La Habana Cuba.
  • Reinaldo Milán Castillo Hospital ClínicoQuirúrgico Hermanos Ameijeiras. La Habana Cuba.
  • Ana Mengana Betancourt Hospital ClínicoQuirúrgico Hermanos Ameijeiras. La Habana Cuba.
  • Suilber Rodríguez Blanco Hospital ClínicoQuirúrgico Hermanos Ameijeiras. La Habana Cuba.
  • Wendy Fusté Pedroso Hospital ClínicoQuirúrgico Hermanos Ameijeiras. La Habana Cuba.

Abstract

Left ventricular noncompaction, also known as "spongiform" cardiomyopathy, is a rare congenital anomaly of myocardial morphology, with deep intertrabecular recesses freely communicated with the ventricular cavity. The case of a 61 year old man, who was admitted to the Cardiology Service for syncope study, is presented. During his admission he underwent an echocardiogram and an isolated left ventricular noncompaction was diagnosed. It was decided to implant an automatic cardioverter-defibrillator in order to prevent potentially fatal malignant ventricular arrhythmias that might trigger his syncopes, after which the patient has progressed favorably.

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Published

2016-07-24

How to Cite

1.
Gutiérrez López A, Ramos Emperador C, Cruz Cardentey M, Milán Castillo R, Mengana Betancourt A, Rodríguez Blanco S, et al. Left ventricular noncompaction apropos of a case. CorSalud [Internet]. 2016 Jul. 24 [cited 2025 Jul. 19];8(3):194-9. Available from: https://revcorsalud.sld.cu/index.php/cors/article/view/142

Issue

Section

CASE REPORTS