Eisenmenger syndrome in an adult patient with dyspnea

Authors

  • Juan S. Theran León
  • Laura Y. Esteban Badillo
  • Luis A. Dulcey Sarmiento

Abstract

Eisenmenger syndrome is the most severe form of pulmonary arterial hypertension associated with congenital heart disease. A non-restrictive left-to-right shunt triggers the development of pulmonary vascular disease, progressive pulmonary arterial hypertension, and an increase in pulmonary vascular resistance that can reach systemic levels. In this article we present the case of a patient with a heart murmur since childhood, who came to a medical consultation due to experiencing shortness of breath with minimal exertion and edema in the lower limbs. The echocardiogram performed revealed the presence of an atrial septal defect with severe pulmonary hypertension, leading to the diagnosis of Eisenmenger syndrome.

Downloads

Download data is not yet available.

References

1. Chaix MA, Gatzoulis MA, Diller GP, Khairy P, Oechslin EN. Eisenmenger Syndrome: A Multisystem Disorder — Do Not Destabilize the Balanced but Fragile Physiology. Can J Cardiol. 2019;35(12):1664-74. DOI: https://doi.org/10.1016/j.cjca.2019.10.002

2. Diller GP, Lammers AE, Oechslin E. Treatment of adults with Eisenmenger syndrome — State of the art in the 21st century: A short overview. Cardiovasc Diagn Ther. 2021;11(4):1190-9. DOI: https://doi.org/10.21037/cdt-21-135

3. Niwa K. Adult Congenital Heart Disease with Pregnancy. Korean Circ J. 2018;48(4):251-76. DOI: https://doi.org/10.4070/kcj.2018.0070

4. Pascall E, Tulloh RM. Pulmonary hypertension in congenital heart disease. Future Cardiol. 2018;14(4):343-53. DOI: https://doi.org/10.2217/fca-2017-0065

5. Arshad HB, Duarte VE. Evaluation and Management of Pulmonary Arterial Hypertension in Congenital Heart Disease. Methodist Debakey Cardiovasc J. 2021;17(2):145-51. DOI: https://doi.org/10.14797/ufej2329

6. van der Bruggen CEE, Tedford RJ, Handoko ML, van der Velden J, de Man FS. RV pressure overload: from hypertrophy to failure. Cardiovasc Res. 2017;113(12):1423-32. DOI: https://doi.org/10.1093/cvr/cvx145

7. Kellish AS, Hakim A, Soal V, Hassinger G, Gable B. Where on the Differential Is Eisenmenger Syndrome in a Patient Without Prior Cardiopulmonary Disease? Cureus [Internet]. 2020 [citado 31 Ene 2023];12(6):e8509. Disponible en: https://doi.org/10.7759/cureus.8509

Published

2022-05-26

How to Cite

1.
Theran León JS, Esteban Badillo LY, Dulcey Sarmiento LA. Eisenmenger syndrome in an adult patient with dyspnea. CorSalud [Internet]. 2022 May 26 [cited 2025 Jul. 1];15(1):72-4. Available from: https://revcorsalud.sld.cu/index.php/cors/article/view/892

Issue

Section

CASE REPORTS